Differential diagnostics of syndrome and non-syndrome forms of dst on the basis of the scale of assessment

Abstract

A systematization of the symptoms of connective tissue dysplasia with a subsequent scoring is suggested in this study. The evaluation is based on the systemic involvement of connective tissue in the pathological process. This serves as a criterion for the severity of dysplasia and helps differentiate the syndrome and non-syndrome forms of connective tissue dysplasia. Constants (2 points) and periodic (1 point) signs of connective tissue dysplasia in children and adolescents, in patients of older age groups were identified. The assessment of dysplasia by both external and internal signs on the part of the reproductive system is supplemented. In this article, the following system of registration of signs of DST in children is suggested: in early age groups (infancy, early age, ie, up to 6 years, when the child does not yet have all the dysplasia syndromes by age), it was suggested to use a scoring only dysplastic symptoms. Since the age of seven, it has been suggested to evaluate dysplasia with the help of syndromes. This evaluation system can be used in any age group, beginning with the early age and ending with the senior age period. The claimed method of diagnosis of DST in children and adults makes it possible to identify the course of this state of connective tissue at earlier stages of the disease, to prescribe corrective therapy. This will slow the progression of manifestations of connective tissue dysplasia later on.