Preview

Ural Medical Journal

Advanced search

Clinical case of multiphasic acute disseminated encephalomyelitis in childhood

https://doi.org/10.25694/URMJ.2018.11.24

Abstract

Acute disseminated encephalomyelitis (ADEM) is a monophasic demyelinating disorder. But 1,8-3,4% of children may develop relapsing disease. We introduced a boy diagnosed with multiphasic ADEM and experienced residual focal neurological deficit. We emphasize the importance of long-term follow-up and recognizing risk factors of relapse in demyelinating disorders.

About the Authors

K. S. Nevmerzhitskaya
ФГБОУ ВО Уральский государственный медицинский университет Минздрава России
Russian Federation


L. I. Volkova
ФГБОУ ВО Уральский государственный медицинский университет Минздрава России
Russian Federation


R. S. Volozhanin
ГАУЗ СО «Областная детская клиническая больница»
Russian Federation


References

1. Absoud M., Lim M.J., Chong W.K. et al. Paediatric acquired demyelinating syndromes: incidence, clinical and magnetic resonance imaging features. Mult Scler. 2013; 19: 76-86.

2. Tanuja Chitnis. Pediatric Multiple Sclerosis and Acute disseminated encephalomyelitis. In: Weiner H.L., Stankiewicz J.M. Multiple Sclerosis: Diagnosis and Therapy, First Edition. John Wiley and Sons, Ltd; 2012: 101-135.

3. Pohl D., Alper G., Van Haren K. et al. Acute disseminated encephalomyelitis. Update on an inflammatory CNS syndrome. Neurology. 2016; 87: 38-45.

4. Suppiej A., Cainelli E., Casara G., Cappellari A., Nosadini M., Sartori S. Long-term neurocognitive outcome and quality of life in pediatric acute disseminated encephalomyelitis. Pediatr Neurol. 2014; 50: 363-7.

5. Banwell B., Arnold D.L., Tillema J.-M. et al. MRI in the evaluation of pediatric multiple sclerosis. Neurology. 2016; 87: 88-96.

6. Huppke P., Rostasy K., Karenfort M., et al. Acute disseminated encephalomyelitis followed by recurrent or monophasic optic neuritis in pediatric patients. Mult Scler.2013; 19: 941-6.

7. Mikaeloff Y., Caridade G., Husson B., Suissa S., Tardieu M. Acute disseminated encephalomyelitis cohort study: prognostic factors for relapse. Eur J Paediatr Neurol. 2007; 11: 90-5.

8. Tenembaum S., Chamoles N., Fejerman N. Acute disseminated encephalomyelitis: a long-term follow-up study of 84 pediatric patients. Neurology. 2002; 59: 1224-31.

9. Kariyawasam S., Singh R.R., Gadian J. Et al. Clinical and radiological features of recurrent demyelination following acute disseminated encephalomyelitis. Mult Scler Relat Disord. 2015; 4(5): 451-6.

10. Krupp L.B., Tardieu M., Amato M.P. et al. International Pediatric Multiple Sclerosis Study Group criteria for pediatric multiple sclerosis and immune-mediated central nervous system demyelinating disorders: revisions to the 2007 definitions. Mult Scler. 2013; 19: 1261-7.


Review

For citations:


Nevmerzhitskaya KS, Volkova LI, Volozhanin RS. Clinical case of multiphasic acute disseminated encephalomyelitis in childhood. Ural Medical Journal. 2018;(11):60-63. (In Russ.) https://doi.org/10.25694/URMJ.2018.11.24

Views: 265


ISSN 2071-5943 (Print)
ISSN 2949-4389 (Online)