Generalized hemangiomatosis as a cause of unintentionable maternal death

Abstract

The article presents the observation of a generalized hemangiomatosis in the puerpera of 28 years. The patient entered the maternity hospital at the gestational age of 39-40 weeks with the clinic of antenatal fetal death, premature detachment of the normally located placenta. In an emergency, she was laparotomy, a Caesarean section. During the subsequent period of the patient's stay in the hospital four operations were performed. In the course of the operations, the uterus and tubes were extirpated for 12 days, splenectomy for 32 hospital stings. Each surgical intervention was accompanied by a significant blood loss (1800 ml, 1500 ml). Despite the resuscitation measures carried out in full, the death of the child was due to the progression of the DIC syndrome. As a result of an autopsy study, the diagnosis "General Disease” was diagnosed with O99.8 generalized hemangiomatosis with uterine and splenic lesions, thrombosis of abnormal vessels of various prescriptions during pregnancy 39-40 weeks. From the standpoint of the doctrine of preventable mortality, this lethal outcome should be considered unacceptable, and clinical diagnosis of generalized hemangiomatosis is difficult due to the absence of cutaneous manifestations of the disease.